ELLIS-VAN CREVELD SYNDROME: REPORT OF A CASE IN AN ADULT PATIENT

Authors

  • ALI ANDON PETROSSIANS From the Cardiovascular Research Center, Shahid Rajaii Heart Hospital, Tehran, Islamic Republic of Iran.
  • MAJID MALEKI
Abstract:

Ellis-van Creveld syndrome is transmitted as an autosomal recessive trait. This syndrome is accompanied in 60% of cases with congenital heart disease, mostly single atrium or large ASD. Patients are mostly symptomatic, but in this rare case despite 68 years of age, the patient was free of symptoms except for complete heart block for which pacemaker was inserted

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Journal title

volume 7  issue 1

pages  59- 60

publication date 1993-05

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